Treatment of cystic fibrosis and other rare lung diseases / ed.: A.Azuma, M.S. Schechter. - Switzerland: Springer, 2017. - 263 p. - (Milestones in drug therapy). - ISBN 978-3-0348-0975-7 Шифр: 01  Место хранения:   01 | ГПНТБ СО РАН | Новосибирск

Оглавление / Contents

Part I. Etiopathology and Genetics of Rare Lung Diseases 1 An Introduction to Clinical Aspects of Cystic Fibrosis ....... 3 Nauman Chaudary and Michael S. Schechter 2 Diffuse Panbronchiolitis .................................... 21 Naoto Keicho and Minako Hijikata 3 Idiopathic Pulmonary Fibrosis ............................... 39 Chiko Shimbori, Pierre-Simon Bellaye, Philipp Kolb, and Martin Kolb 4 Pulmonary Alveolar Proteinosis: A Historic Perspective ...... 71 Koh Nakata and Ryushi Tazawa 5 Lymphangioleiomyomatosis .................................... 87 Kuniaki Seyama Part II. Treatment of Cystic Fibrosis 6 CFTR Modulator Therapies in Cystic Fibrosis ................ 101 David R. Spielberg, John P. Clancy, and Christopher Siracusa 7 Drug Therapies that Augment Airway Surface Liquid .......... 119 Evangelia Daviskas, Sheila Sivam, Mark R. Elkins, Tiffany J. Dwyer, Ruth Dentice, and Peter T. Bye 8 Anti-Inflammatory Therapies for Cystic Fibrosis ............ 139 Elliott C. Dasenbrook and James F. Chmiel 9 Anti-Infective Therapies in Cystic Fibrosis ................ 153 Patrick A. Flume and Donald R. VanDevanter Part III. Treatment of Other Rare Lung Diseases 10 Diffuse Panbronchiolitis: Long-Term Low-Dose Macrolide Therapy .................................................... 173 Mutsuo Yamaya, Arata Azuma, and Shoji Kudoh 11 Idiopathic Pulmonary Fibrosis .............................. 189 Paolo Spagnolo 12 Treatment of Pulmonary Alveolar Proteinosis ................ 211 Muhammad Muhye-ud-din Sheikh and Bruce C. Trapnell 13 Treatment of Lymphangioleiomyomatosis (LAM) ................ 239 Mariam Anis and Francis X. McCormack